Frontotemporal dementia is a relatively rare dementia syndrome characterised by insidious and progressive changes in behaviour and personality. Currently, no disease-modifying treatment or cure exists, and differential diagnosis is challenging. In this webinar we will provide an overview of current clinical recommendations for the diagnosis of behavioural-variant frontotemporal dementia, with a focus on differentiation from Alzheimer’s disease and from primary psychiatric disorders. We will also outline assessment approaches for the diagnosis of primary progressive aphasias. We will discuss recent studies examining cross-linguistic studies in primary progressive aphasia and how bilingualism can influence the clinical phenotype. How to approach diagnosis in a low resource setting will be considered. Finally, we will provide an overview of available management and treatment options.